Polyarteritis with lung involvement [Churg-Strauss]/EGPA
Description
Churg-Strauss syndrome: Eosinophilic granulomatosis with polyangiitis (EGPA), previously known as Churg-Strauss syndrome, is a systemic vasculitis of small-to medium vessels, characterized by asthma, transient pulmonary infiltrates, and hypereosinophilia.
Data source
| FinnGen phenocode | M13_CHURGSTRAUSS |
| Hospital Discharge registry | ICD-10: M301, ICD-9: 4460B |
| Cause of Death registry | ICD-10: M301, ICD-9: 4460B |
| Level in the ICD-hierarchy | 4 |
| First defined in version | DF2 |
Key figures
| Sex | All | Female | Male |
| Number of individuals | 33 | 23 | 10 |
| Unadjusted prevalence (%) | 0.02 | 0.02 | 0.01 |
| Mean age at first event (years) | 47.42 | 48.06 | 45.94 |
| Case fatality at 5-years (%) | 6.06 | 4.35 | 10.0 |
Longitudinal metrics
| Sex | All | Female | Male |
| Median nb. of events per indiv. | 10 | 7 | 16 |
| Recurrence at 6 months (%) | 63.64 | 56.52 | 80.0 |
Associations
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