Behçet disease

Description

Behcet's syndrome: Bechet disease (BD) is a chronic, relapsing, multisystemic vasculitis characterized by mucocutaneous lesions, as well as articular, vascular, ocular and central nervous system manifestations.

Data source
FinnGen phenocode M13_BEHCET
Hospital Discharge registry ICD-10: M352
Cause of Death registry ICD-10: M352
Level in the ICD-hierarchy 4
First defined in version DF2
Ontology
DOID 13241
GWAS catalog 0003780
MESH D000074079
SNOMED CT 310701003

Key figures

Sex All Female Male
Number of individuals 33 24 9
Unadjusted prevalence (%) 0.02 0.02 0.01
Mean age at first event (years) 49.64 49.81 49.21
Case fatality at 5-years (%) 6.06 8.33 0.0

Longitudinal metrics

Sex All Female Male
Median nb. of events per indiv. 2 3 1
Recurrence at 6 months (%) 54.55 62.5 33.33

Associations

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