Cicatricial pemphigoid

Description

mucous membrane pemphigoid: Mucous membrane pemphigoid is a bullous dermatosis characterised clinically by blistering of the mucous membranes followed by scarring, and immunologically by IgG, IgA and/or C3 deposits on the epidermal basement membrane.

Data source
FinnGen phenocode L12_PEMPHIGOID_CICA
Hospital Discharge registry ICD-10: L121
Cause of Death registry ICD-10: L121
Level in the ICD-hierarchy 4
First defined in version DF2
Ontology
DOID 11656
GWAS catalog 1000680
MESH D010390
SNOMED CT 76092003

Key figures

Sex All Female Male
Number of individuals 21 15 6
Unadjusted prevalence (%) 0.01 0.02 0.01
Mean age at first event (years) 60.29 60.93 58.71
Case fatality at 5-years (%) 0.0 0.0 0.0

Longitudinal metrics

Sex All Female Male
Median nb. of events per indiv. 3 3 6
Recurrence at 6 months (%) 57.14 53.33 66.67

Associations

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