Other and unspecified polyneuropathies, also in other diseases

Description

chronic inflammatory demyelinating polyradiculoneuropathy: A slowly progressive autoimmune demyelinating disease of peripheral nerves and nerve roots. Clinical manifestations include weakness and sensory loss in the extremities and enlargement of peripheral nerves. The course may be relapsing-remitting or demonstrate a step-wise progression. Protein is usually elevated in the spinal fluid and cranial nerves are typically spared. GUILLAIN-BARRE SYNDROME features a relatively rapid progression of disease which distinguishes it from this condition. (Adams et al., Principles of Neurology, 6th ed, p1337)

Data source
FinnGen phenocode G6_POLYOTHUNS
Hospital Discharge registry ICD-10: G618/G619/G629/G611/G628/G63, ICD-8: 3540[8-9]
Cause of Death registry ICD-10: G611/G629/G619/G63/G618/G628, ICD-8: 3540[8-9]
Level in the ICD-hierarchy 3
First defined in version DF2
Ontology
DOID 5213
GWAS catalog 1000868
MESH D011115
SNOMED CT 128209004

Key figures

Sex All Female Male
Number of individuals 1967 835 1132
Unadjusted prevalence (%) 1.13 0.84 1.51
Mean age at first event (years) 60.16 58.82 61.15
Case fatality at 5-years (%) 6.76 4.67 8.3

Longitudinal metrics

Sex All Female Male
Median nb. of events per indiv. 2 2 2
Recurrence at 6 months (%) 44.74 45.27 44.35

Associations

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