Amyloidosis, other/unspecified

Description

amyloidosis: A disorder characterized by the localized or diffuse accumulation of amyloid protein in various anatomic sites. It may be primary, due to clonal plasma cell proliferations; secondary, due to long standing infections, chronic inflammatory disorders, or malignancies; or familial. It may affect the nerves, skin, tongue, joints, heart, liver, spleen, kidneys and adrenal glands.

Data source
FinnGen phenocode E4_AMYLNAS
Hospital Discharge registry ICD-10: E859, ICD-8: 27699
Cause of Death registry ICD-10: E859, ICD-8: 27699
Level in the ICD-hierarchy 4
First defined in version DF2
Ontology
DOID 9120
GWAS catalog 1001875
MESH D000686
SNOMED CT 17602002

Key figures

Sex All Female Male
Number of individuals 137 75 62
Unadjusted prevalence (%) 0.08 0.08 0.08
Mean age at first event (years) 59.62 57.39 62.31
Case fatality at 5-years (%) 21.9 22.67 20.97

Longitudinal metrics

Sex All Female Male
Median nb. of events per indiv. 4 5 2
Recurrence at 6 months (%) 59.12 64.0 53.23

Associations

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