Dermatopolymyositis (FG)
Description
juvenile dermatomyositis: Juvenile dermatomyositis (JDM) is the early-onset form of dermatomyositis (DM, see this term), a systemic, autoimmune inflammatory muscle disorder, characterized by proximal muscle weakness, evocative skin lesion, and systemic manifestations.
Data source
| FinnGen phenocode | DERMATOPOLY_FG |
| Include | M13_DERMATOMYOTH, M13_POLYMYO, M13_DERMATOPOLYNAS |
| First defined in version | DF2 |
Key figures
| Sex | All | Female | Male |
| Number of individuals | 146 | 105 | 41 |
| Unadjusted prevalence (%) | 0.08 | 0.11 | 0.05 |
| Mean age at first event (years) | 52.78 | 52.33 | 53.94 |
| Case fatality at 5-years (%) | 6.85 | 5.71 | 9.76 |
Longitudinal metrics
| Sex | All | Female | Male |
| Median nb. of events per indiv. | 3 | 3 | 3 |
| Recurrence at 6 months (%) | 60.27 | 60.95 | 58.54 |
Associations
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