Biliary chirrosis, primary

Description

primary biliary cirrhosis: Primary biliary cholangitis (PBC) is a chronic and slowly progressive cholestatic liver disease of autoimmune etiology characterized by injury of the intrahepatic bile ducts that may eventually lead to liver failure.

Data source
FinnGen phenocode CHIRBIL_PRIM
Hospital Discharge registry ICD-10: K743
Cause of Death registry ICD-10: K743
First defined in version DF2
Ontology
DOID 12236
GWAS catalog 1001486
MESH D008103
SNOMED CT 31712002

Key figures

Sex All Female Male
Number of individuals 201 176 25
Unadjusted prevalence (%) 0.12 0.18 0.03
Mean age at first event (years) 56.54 56.45 57.18
Case fatality at 5-years (%) 3.98 3.41 8.0

Longitudinal metrics

Sex All Female Male
Median nb. of events per indiv. 7 7 6
Recurrence at 6 months (%) 78.11 78.98 72.0

Associations

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