Malignant neoplasm of peripheral nerves and autonomic nervous system


tumour of cranial and spinal nerves: ['A benign or malignant neoplasm arising from a peripheral nerve or the perineural sheaths.', 'Neoplasms which arise from peripheral nerve tissue. This includes NEUROFIBROMAS; SCHWANNOMAS; GRANULAR CELL TUMORS; and malignant peripheral NERVE SHEATH NEOPLASMS. (From DeVita Jr et al., Cancer: Principles and Practice of Oncology, 5th ed, pp1750-1)']

Data source
Cause of Death registry ICD-10: C47, ICD-8: 192[4-5]
Cancer reg: TOPOGRAPHY codes C47
Level in the ICD-hierarchy 3
First defined in version DF4
DOID 1192
GWAS catalog 0002431
MESH D010524

Key figures

Sex All Female Male
Number of individuals 14 6 8
Unadjusted prevalence (%) 0.01 0.01 0.01
Mean age at first event (years) 37.63 31.09 42.53
Case fatality at 5-years (%) 14.29 16.67 12.5

Longitudinal metrics

Sex All Female Male
Median nb. of events per indiv. 1 1 1
Recurrence at 6 months (%) - - -


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