Wegener granulomatosis

Description

Granulomatosis with Polyangiitis: A small-vessel necrotizing vasculitis characterised by the association of inflammation of the vessel wall and peri- and extravascular granulomatosis.

Data source
FinnGen phenocode M13_WEGENER
Hospital Discharge registry ICD-10: M313, ICD-8: 4462
Cause of Death registry ICD-10: M313, ICD-8: 4462
Level in the ICD-hierarchy 4
First defined in version DF2
Ontology
DOID 12132
GWAS catalog 0005297
MESH D014890
SNOMED CT 195353004

Key figures

Sex All Female Male
Number of individuals 166 89 77
Unadjusted prevalence (%) 0.1 0.09 0.1
Mean age at first event (years) 52.28 51.06 53.68
Case fatality at 5-years (%) 3.61 3.37 3.9

Longitudinal metrics

Sex All Female Male
Median nb. of events per indiv. 9 6 14
Recurrence at 6 months (%) 72.89 68.54 77.92

Associations

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